Compensatory movements during functional activities in ambulatory children with Duchenne muscular dystrophy.

نویسندگان

  • Joyce Martini
  • Mariana Callil Voos
  • Michele Emy Hukuda
  • Maria Bernadete Dutra de Resende
  • Fátima Aparecida Caromano
چکیده

OBJECTIVE During the transitional phase (ambulatory to non-ambulatory), synergies characterize the evolution of Duchenne muscular dystrophy (DMD). This study was performed to describe and quantify compensatory movements while sitting down on/rising from the floor and climbing up/down steps. METHOD Eighty videos (5 children × 4 assessments × 4 tasks) were recorded quarterly in the year prior to gait loss. Compensatory movements from the videos were registered based on the Functional Evaluation Scale for DMD. RESULTS The most frequently observed compensatory movements were upper limb support on lower limbs/floor/handrail during all the tasks and lumbar hyperlordosis, trunk support on handrail, equinus foot, increased base of support, non-alternated descent, and pauses while climbing up/down steps. CONCLUSION Climbing up/down steps showed a higher number of compensatory movements than sitting down on/rising from the floor, which seemed to be lost before climbing up/down steps in ambulatory children with DMD.

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عنوان ژورنال:
  • Arquivos de neuro-psiquiatria

دوره 72 1  شماره 

صفحات  -

تاریخ انتشار 2014